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Talassemiya — autosomal resessiv gemoglobinopatiya; major va minor turlari mavjud. Talassemiya major (Kuuli anemiya): og‘ir mikrotsitar gemolitik anemiya, doimiy transfuzion terapiya, temir ortishi (hemochromatosis), kuchli splenomegaliya va gipersplenizm; splenektomiya va temir chelatatsiya zarur bo‘lishi mumkin
#anemiya#talassemiya#gemoglobinopatiya
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